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Pediatrics Neoplasms of the Kidney 0359c5c0

Wilm's Tumour is associated with all. Except -

A
Hemihypertrophy
B
Beckwith syndrome
C
Aniridia
D
Polycystic kidney
High-Yield Explanation
Ans. is 'd' Polycystic kidney disease (Ref O.P. Ghai, 5/e, p 466; CPDT, 15/e, p 808, Nelson 17/e, 617, 1749 1750,1757)Important associated malformations: syndromes associated with wilm's tumor.Aniridia*Hemihypertrophy*GenitourinaryCryptorchidism*Hypospadias*Gonadal dysgenesis*Pseudohermaphroditism *Horseshoe kidney *Beckwith Wiedemann syndrome*Dr ash syndromeWAGR syndrome*Wilms tumourAniridiaAmbiguous genitaliaMental retardation

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