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Pediatrics General fc3686ef

Mousy odour urine is seen in-

A
Maple syrup urine
B
Phenylketonuria
C
Isovalericaciduria
D
Cystinuria
High-Yield Explanation
Ans. is 'b' i.e., Phenylketonuria Inborn Errors of amino acid metabolism associated with peculiar odor

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