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Medicine Endocrinology f18fbb99

Which of the following are the extraintestinal manifestations of Sipple syndrome?

A
Cutaneous lichen
B
Amylodosis
C
Hirschsprung disease
D
All the above
High-Yield Explanation
Ans. is 'd' i.e., All the aboveMultiple Endocrine Neoplasia (MEN) Syndromes MEN I(Werner syndrome)MEN 2A(Sipple syndrome)MEN 2BPituitaryAdenomas, Hyperplasia----ParathyroidHyperplasiaAdenomasHyperplasia or adenoma--Pancreatic isletsHyperplasiaAdenomasCarcinomas----AdrenalCortical hyperplasiaPheochromocytomaPheochromocytomaThyroid--C-cell hyperplasiaMedullary carcinomaC-cell hyperplasiaMedullary carcinomaExtraendocrine* Foregut carcinoid* Subcutaneous or visceral* Dermal angiofibroma or collagenomaCutaneous lichen amyloidosisHirschsprung diseaseMucosal and gastro intestinal neuroma, ganglio-neuromas,Marfanoid habitusMutant gene locusMEN IRETRET

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