Highest mortality in pregnancy
High-Yield Explanation
Eisenmenger syndrome
These patients have pulmonary hypertension with shunt (right to left) through an open ductus or ASD or VSD.
Maternal mortality is high i.e. 50% & so is a perinatal loss (50%).
Fallot’s tetralogy, coarctaion of aorta & Marfan's syndrome hav mortality’ rate of 5-10%, 3-9% & 25% respectively