Ebstein anomaly is associated with all of the following Except
High-Yield Explanation
EBSTEIN'S ANOMALY:Ebstein's anomaly is due to the abnormal downward displacement of tricuspid valve into the right ventricle.Tricuspid valve has 3 leaflets- anterior, posterior and septalAnterior leaflet of valve retains attached to valve ring and the other two leaflets displaced downwards.HEMODYNAMICS:The displaced tricuspid valve divides the right ventricle into two poions namely- thin atrialized ventricle and the small normal right ventricle.The effective output from the right side of the hea is decreased because of the combination of poorly functioning small right ventricle, tricuspid valve regurgitation and obstruction to right ventricular outflow due to the large sail-like anterior cuspBlood flows from right atrium to left atrium through patent foramen ovale or ASD results in RIGHT TO LEFT SHUNT-CYANOSISEbstein's anomaly is a ductal dependant(PDA) pulmonary flow cardiac disease.CLINICAL FEATURES:CyanosisParoxysmal attack of tachycardiaDyspnea on exeionSIGNS:Holosystolic murmur due to tricuspid regurgitationMassive cardiomegaly-BOX SHAPED CARDIOMEGALYECG- tall, broad P waves.