Pathology General e19a9ce6 Other than pemphigus, Nikolsky's sign is positive in: A Familial benign chronic pemphigus B Hailey- Hailey disease C Epidermolysis bullosa D All of the above High-Yield Explanation “Nikolsky's sign” is positive in: Pemphigus. Familial benign chronic pemphigus (hailey-hailey disease). Recessive dystrophic epidermolysis bullosa .