Cogan Syndrome is associated with all Except

Cogan's syndrome is characterized by interstitial keratitis together with vestibulo-auditory symptoms. It may be associated with a systemic vasculitis, paicularly aoitis with the involvement of the aoic valve. Glucocoicoids are the mainstay of treatment. Initiation of treatment as early as possible after the onset of hearing loss improves the likelihood of a orable outcome.Ref: Harrison&;s Principles of Internal Medicine; 19th edition; Chapter 385 The Vasculitis Syndromes; Page no: 2193