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Biochemistry Proteins and Amino Acids e124f599

Smell of sweaty feet is seen in:

A
MSUD
B
Phenyl ketonuria
C
Homocystinuria
D
Glutaric acidemia
High-Yield Explanation
Ans. D. Glutaric AcidemiaPeculiar odours in different Amino aciduriasInborn Error of MetabolismUrine OdorGlutaric acidemia (type II)Sweaty feet, acridHawkinsinuriaSwimming PoolIsovaleric AcidemiaSweaty feet, Acrid3-Hydroxy-3- methylglutaric acid uriaCat urineMaple syrup urine diseaseMaple syrupHypermethioninemiaBoiled cabbageMultiple carboxylase deficiencyTomcat urineOasthouse urine diseaseHops-likePhenylketonuriaMousey or mustyTrimethylaminuriaRotting fishTyrosinemiaBoiled cabbage, rancid butter

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