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Pediatrics C.V.S. df7d4781

Fanconi's anemia is a:

A
Constitutional anemia
B
Hemolytic anemia
C
Iron deficiency anemia
D
Auto-immune anemia
High-Yield Explanation
a. Constitutional anemia(Ref: Nelson's 20/e p 2390-2392, Ghai 8/e p 349-351)Constitutional pancytopenia is defined as decreased marrow production of the 3 major hematopoietic lineages on an inherited basis, resulting in anemia, neutropenia and thrombocytopenia. Important causes are:Fanconi anemiaAmegakaryocytic thrombocytopeniaShwachman-Diamond syndromeDown syndromeDyskeratosis congenitaNoonan syndrome

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