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Medicine Genetics de11a9b4

Cystic fibrosis affects all systems EXCEPT:

A
Respiratory
B
Endocrine
C
Hepatobiliary
D
Genitourinary
High-Yield Explanation
ANSWER: (B) EndocrineREF: Harrison's Internal Medicine, Chapter 253, Davidson's internal medicine 20tSl edition page- 685FEATURES OF CYSTIC FIBROSIS:A- Autosomal recessiveB- BronchiectasisC- Chloride channel block/Ciliary dysfunctionD- Diabetes mellitusE- Exocrine pancreatic failure (>90% of patients with CF)F- Fat malabsorption (steatorrhoea)G- Gall stone/Gene mutation on chromosome 7H- Hepatic cirrhosis/HemoptysisI- Intestinal obstruction/Infertility

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