Pediatrics Disorders of Carbohydrate Metabolism d7af0b5d Which disorder of carbohydrate metabolism typically has cardiac involvement? A Glycogen Storage Disease Type I (Von Gierke disease) B Glycogen Storage Disease Type II (Pompe disease) C Hereditary fructose intolerance D Galactosemia High-Yield Explanation Pompe disease: coarse facies hepatomegaly, hypotonia progressive cardiomegaly and cardiac dysfunction ECG- sho PR, large QRS complexes.