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Pediatrics Adrenal Gland d54c422e

2 weeks old baby having scrotal pigmentation along with hyponatremia, gypoglycemia and hyperkalemia enzyme deficient-

A
11 beta hydroxylase
B
21 a- hydroxylase
C
3- Beta hydroxylase dehydrogenase
D
17- hydroxylase deficiency
High-Yield Explanation
Ans. is 'b' i.e., 21 a- hydroxylase Congenital adrenal hyperplasia (CAH)o Autosomal recessive disorder,o MC. is a-hvdroxylase deficiency.In 21a-hyroxylese deficiencyo There is deficiency of mineralocorticoids & glucocorticoid,o This leads to hypoglycemia, hyponatremia.

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