About Mayer rokitansky kuster hauser syndrome
High-Yield Explanation
Mayer Rokitansky Kuster Hauser syndrome ; Mullerian Agenesis (karyotype;46XX) (Phenotype female) Vagina,Uterus,Fallopian tubes absent. Typically ovaries are normal Secondary sexual characters are well developed May be associated with urologic anomalies and Skeletal malformations Management; 1.Frank dilatation 2.Vaginoplasty (Mc Indoe operation or Williams vaginoplasty) Ref: Clinical Gynecologic Endocrinology and Infeility; Eigth Edition, Chapter 9