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Microbiology General d101b2e0

Which of the following is not prion associated disease: March 2011

A
Scrapie
B
Kuru
C
Creutzfeldt-jakob disease
D
SSPE
High-Yield Explanation
Scrapie latrogenic Creutzfeldt -Jakob disease ; Infection from prion contaminated human growth hormone, duramater graft, corneal transplant Kuru (human):Infection through ritualistic cannibalism Variant (CJD):Infection from bovine prion (Eating BSE infected beef) Familial CJD:Germline mutation in PRNP Sporadic CJD:Somatic mutation or spontaneous convention of PRPc into PRPsc Fatal familial insomnia:Germline mutation in PRNP Gestmann Strausster Scheinker:Germline mutation in PRNP Bovine spongiform encephalopathy Transmissible mink encephalopathy

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