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Ophthalmology Miscellaneous cce47d7a

Aniridia is associated with -

A
Retinoblastoma
B
Hepatoblastoma
C
Nephroblastoma
D
Medulloblastoma
High-Yield Explanation
Congenital aniridia (Iridremia) -Refers to congenital absence of iris (true aniridia) i.e., complete absence of iris is extremely rare. Usually, a peripheral rim of iris is present and this condition is called Clinical aniridia. This may be associated with glaucoma due to angle anomalies. It is associated with nephroblastoma (Wilms tumour) WAGR syndrome- Wilms tumour Aniridia Genitourinary anomalies mental Retardation.

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