Deafness is seen with: (Repeat)

Ans: B (Congenital QT syndrome) Ref: Diseases of the Ear Nose and Throat by PL Dhingra.5th edn ,2010Page 129Explanation:Congenital deafness associated syndromesJervell and Lange-Nielsons syndromeAutosomal recessiveRepeated syncopal attacksCongenita] sensorineural hearing lossProlonged QT in ECGAlports syndromeAutosomal dominant or X linkedDelayed onset of sensorineural hearing lossHereditary progressive glomerulonephritisCorneal dystrophyPend red syndromeAutosomal recessiveCongenital SNHLGoitreUsher syndromeAutosomal recessiveDelayed onset of SNHLRetinitis pigmentosaNight blindnessTreacher Collin syndrome and Aperts syndrome are associated with conductive hearing loss