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Biochemistry Phospholipids, Glycolipids and their disorders c5123274

In Gaucher's diseases, there is deficiency of -

A
Glucocerebrosidase
B
Glucokinase
C
Sphingomyelinase
D
G-6PD
High-Yield Explanation
Ans. is 'a' i.e., Glucocerebrosidase o Gaucher's disease is due to deficiency of (3-glucosidase (glucocerebrosidase).o This question is repeat front AH MS 97.DiseaseEnzyme deficiencyLipid accumulatedTay-sach diseaseHexosaminidase AGM, gangliosideSandoff diseaseHexosaminidase BGM,gangliosideNiemann-Pick diseaseSphi ngomyel inaseSphingomyelineFarber's diseaseCeram idaseAcyl-sphingosine (ceramide)Fabry's diseasea-galactosidaseGlobotri sy IceramideKrabbe's diseaseb-galactosidase(Galactosylceramidase)GalactosvlceramideGaucher's diseaseb-gl ucosidase (gl ucoccrebrosi dase)Glueosy IceramideMetachromatic leukodystrophyArylsulfatase A3-Suffoga!actosy!ceramide

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