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Pathology Genetics c4fca4c4

Which is the most common tumor associated with type I neurofibromatosis?

A
Optic nerve glioma
B
Meningioma
C
Acoustic schwannoma
D
Low grade astrocytoma
High-Yield Explanation
Ans. (a) Optic nerve glioma(Ref: Robbins 9th/pg 298)NF1 patients have increased risk of Meningioma Q, Pheochromocytoma Q & Wilm's Tumor QMost common tumor in NF1 is optic nerve glioma QMost common Leukemia in NF1 is JMML Q (Juvenile Myelomonocytic Leukemia)

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