Enzyme defective in Maple syrup urine disease is:
High-Yield Explanation
Enzyme deficiencies and conditionsTyrosinase is deficient in albinismPhenylalanine hydroxylase is deficient in phenylketonuriaMaple syrup urine disease is due to a defect in the enzyme branched chain alpha-keto acid dehydrogenaseHomogentisate oxidase is deficient in alkaptonuria