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Biochemistry Proteins and Amino Acids abd04190

Type I Tyrosinemia is caused by:

A
Tyrosine transaminase
B
Fumarylacetoacetate hydrolase
C
4 Hydroxy phenyl pyruvate hydroxylase
D
Maleyl acetoacetate isomerase
High-Yield Explanation
Ans. B. Fumarylaceto Acetate HydrolaseAmino acidurias and enzyme defectClassic Phenyl KetonuriaPhenylalanine HydroxylaseAlkaptonuriaHomogentisate OxidaseTyrosinemia Type I (Most common Tyrosinemia)Fumaryl Aceto Acetate HydrolaseTyrosinemia Type IITyrosine TransaminaseTyrosinemia Type IIIPara Hydroxy Phenyl Pyruvate hydroxylase/Para hydroxyl Phenyl Pyruvate DioxygenaseHawkinsinuriaPara Hydroxy Phenyl Pyruvate hydroxylase/Para hydroxyl Phenyl Pyruvate Dioxygenase is mutant, so that it catalyse only partial reaction.Segawa SyndromeGTP CyclohydrolaseAlbinismTyrosinase

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