Which is not true about Sturge weber syndrome -
High-Yield Explanation
Sturge Weber Syndrome
It is one of the hereditary neurocutaneous syndromes
Characterized by :
A large unilateral cutaneous angioma (port wine stain) of the face
Angiomas in the brain involving the ipsilateral cerebral hemisphere and meninges.
Adrenal pheochromocytoma
Cerebral angioma leads to cortical atrophy
The angiomas are visible radiologically due to its characteristic linear rail-track or tram-track calcification.
Intracranial hamartomas are seen in another neurocutaneous syndrome → tuberous sclerosis (Bournevilles ds)