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Pediatrics Disorders of Carbohydrate Metabolism a0c74c0e

Which glycogen storage disease (GSD) does not affect muscles?

A
Type I
B
Type II
C
Type III
D
Type V
High-Yield Explanation
Type I GSD (Von Gierke disease) is a liver glycogenoses i.e. involves liver Type 2 (Pompe disease), type V (McArdles disease) and type VII ( Tarui disease) involves muscles (Muscle Glycogenoses) Type 3 GSD (Cori's disease) is predominantly a liver glycogenoses but skeletal muscle involvement may also be seen.

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