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Medicine Bronchiectasis 9d1c6c02

Infeility in Kaagener syndrome is due to?

A
Oligospermia
B
Blockage of epididymis
C
Asthenospermia
D
Undescended testis
High-Yield Explanation
Asthenospermia or poor sperm motility is due to missing dynein arms, which is the basic defect of Kaagener's syndrome. It is a ciliopathic, autosomal recessive genetic disorder. Around 90% of individuals with kaagener's have ultrastructural defects affecting protein(s) in the outer and/or innerdynein arms. Triad consist of:- - situs inversus - chronic sinusitis - bronchiectasis.

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