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Biochemistry Proteins and Amino Acids 9b66dcd0

Deficiency of arginosuccinate synthase causes-

A
Citrullinemia
B
Hyperargininemia
C
Argininosuccinic aciduria
D
Type I hyperammonemia
High-Yield Explanation
Ans. is 'a' i.e., CitrullinemiaDisorders caused by genetic defects of urea cycle enzymesDisordersDefective enzymeProducts accumulatedHyperammonemia type-ICarbamoyl phosphate synthase-IAmmoniaHyperammonemia type-IIOrnithine transcarbamoylaseAmmoniaCitrullinemiaArgininosuccinate synthaseCitrullineArgininosuccinic aciduriaArgininosuccinate lyaseArgininosuccinateArgininemiaArginaseArginine

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