Pathology Genetics 96f29da9 Enzyme deficiency in Hunter disease is: A L-iduronidase B Iduronate sulfatase C Heparan sulfamidase D Hyaluronidase High-Yield Explanation Ans. (b) Iduronate sulfatase(Ref: Robbins 9th/pg 154-155)All Mucopolysaccharidoses are autosomal recessive except Hunter's disease which is X linked recessive Q