True about primary lymphedema: a) Prevalence is 2% b) Onset b/w 2-35 years indicates lymphedema tarda c) Onset >35 yrs indicates praecox type d) Associated with Milroy's disease e) Lymphangiosarcoma may occur

"The primary lyrnphedemas are relatively uncommon, occurring in 1 of every 10,000 individuals"-Sabiston "Lymphangiosarcoma is a rare tumor that develops as a complication of long-standing (usually more than 10 years) lymphedema."- Sabiston "Cutaneous lymphangiosarcoma may develop in chronically lymphedematous extremities."- Devita 8/e Chapter 45