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Medicine Cystic fibrosis & Sleep apnea 8cf9b800

Kaagener syndrome is not associated with?

A
Situs inversus
B
Subluxation of lens
C
Bronchiectasis
D
Sinusitis
High-Yield Explanation
Kaagener syndrome /Immotile cilia syndrome is a AR genetic disorder that causes a defect in action of cilia . Triad includes Bronchiectasis , sinusitis and situs inversus. In males it leads to immotility of sperms causing infeility . There is also marked reduction in feility in female sufferers. There is also impaired ciliary function leading to reduced mucus clearance from lungs and susceptibility to chronic recurrent respiratory infections .

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