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Biochemistry General 6fbf8de4

Orotic aciduria is due to deficiency of ?

A
Decarboxylase
B
Tyrosinase
C
Isomerase
D
Homogentisate oxidase
High-Yield Explanation
Ans. is 'a' i.e., Decarboxylase Metabolic disease Enzyme deficient Maple syrup urine disease Branched chain ketoacid dehydrogenase Methyl-melonic aciduria Methyl-malonyl CoA mutase (isomerase) Isovaleryl-CoA dehydrogenase Sweaty feet odor in body Tyrosinemia I (Tyrosinosis) Fumarylacetoacetate hydroxylase Tyrosinemia II Tyrosine transaminase (Tyrosine aminotransferase) Neonatal tyrosinemia Hydroxyphenyl pyruvate hydroxylase Albinism Tyrosinase Alkaptonuria Homogentisate oxidase Phenylketonuria Phenylalanine hydroxylase Orotic aciduria Homocystinuria Lesh-Nyhan syndrome Cystinosis OMP decarboxylase Cystathionine synthatase Complete deficiency of enzyme HGP Cystine reductase

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