Amino acids excreted in the urine in cystinosis

Cystinuria is one of the inborn error of metabolism included in Garrod&;s tetrad. It is an autosomal recessive condition. The disorder is attributed to the deficiency in transpo of amino acids. There will be abnormal excretion of cystine and to a lesser extent lysine, ornithine and arginine. Hence the condition is also called cystine-lysuriaRef: DM Vasudevan - Textbook of Biochemistry for Medical Students, 7th edition, page no: 219