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Pediatrics General 500e09b3

Kaagener syndrome all true except?

A
Bronchitis
B
Sinusitis
C
Bronchiectasis
D
Infeility
High-Yield Explanation
Ans. is 'a' i.e., Bronchitis Kaagener syndrome is a subset of primary ciliary dyskinesia, an autosomal recessive condition characterized by abnormal ciliary structure and/or function leading impaired mucociliary clearance. Clinical presentation Kaagener syndrome is characterised by the clinical triad of 1 Situs inversus Chronic sinusitis and/or nasal polyposis Bronchiectasis Other features include Telecanthus: widened interpupillary distance by a nasal polyp Infeility in males Subfeility in females

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