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Pathology Bilirubin Metabolism 40cfd5da

Primary biliary cirrhosis is most commonly associated with______

A
Systemic sclerosis
B
Sjogren syndrome
C
Ulcerative colitis
D
Pancreatitis
High-Yield Explanation
Primary Biliary Cirrhosis Autoimmune disorder Clinical manifestation - obstructive jaundice F > M Antibody seen in antimitochondrial ab which is formed against E2 subunit of PDH enzyme. Interlobular bile ducts are actively destroyed by lymphoplasmacytic inflammation with or without granulomas.

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