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Biochemistry Metabolism of carbohydrate 40209a49

Enzyme deficiency in McArdle's syndrome?

A
Acid maltase
B
Muscle phosphorylase
C
Liver debranching enzyme
D
Branching enzyme
High-Yield Explanation
Type name Enzyme Deficiency Clinical Features V Myophosphorylase deficiency, McArdle's syndrome Muscle phosphorylase Poor exercise tolerance Muscle glycogen abnormally high (2.5%-4%) Blood lactate very low after exercise Reference: Harper; 30th edition; Table: 18-2; Page no: 179

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