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Medicine Polycystic Kidneys 3f114ea0

Distal and collecting duct cysts are seen in?

A
ADPKD
B
ARPKD
C
Tuberous sclerosis
D
Nephronophthisis
High-Yield Explanation
ADPKD: cysts are in coex & medulla (Hepatic cyst manifestation) ARPKD: Distal & Collecting duct cyst (Hepatic fibrosis) MC age- <1yr Protein affected- Fibrocystin(Chr. 6) Presentation- B\L Abdominal mass Hypolasia of lungs Peripoal fibrosis

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