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Biochemistry Nutrition & Digestion 3f04a775

A child with kinky hair, intellectual disability, seizures. What is the diagnosis?

A
Down's syndrome
B
Menke's disease
C
Iron deficiency anemia
D
Lesch Nyhan syndrome
High-Yield Explanation
Ans. B. Menke's DiseaseMenke's (Kinky or Steely) Hair SyndromeMutation in ATP7A geneX-linked recessive conditionDefective Copper binding P type ATPaseCopper is not mobilised from Intestine.Deficiency of Xanthine oxidase.

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