Marie and Sainton's disease is also known as:
High-Yield Explanation
Important Mainfestations of cleidocranial dysostosis or Marie and Sainton's disease:
Partial or complete absence of clavicles.
Delayed closure of fontanelle.
Wormian bones are common.
The sagittal suture is characteristically sunken, giving the skull a flat appearance.
Hypoplasia of maxilla.
Prolonged retention of deciduous teeth (AP-14) and subsequent delay in eruption of succedaneous teeth.
Absence or paucity of cellular cementum on the roots of the permanent teeth with no increased thickening of the primary acellular cementum.