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Pathology General 39043500

Marie and Sainton's disease is also known as:

A
Dentinogenesis imperfecta.
B
Cleidocranial dysostosis.
C
Turners hypoplasia.
D
Amelogenesia imperfecta.
High-Yield Explanation
Important Mainfestations of cleidocranial dysostosis or Marie and Sainton's disease: Partial or complete absence of clavicles. Delayed closure of fontanelle. Wormian bones are common. The sagittal suture is characteristically sunken, giving the skull a flat appearance. Hypoplasia of maxilla. Prolonged retention of deciduous teeth (AP-14) and subsequent delay in eruption of succedaneous teeth. Absence or paucity of cellular cementum on the roots of the permanent teeth with no increased thickening of the primary acellular cementum.

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