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Biochemistry Lipids 38259c8b

Which enzyme defect causes Tay Sach's disease?

A
b glucosidase
B
a galactosidase
C
Hexosaminidase A
D
B galactosidase
High-Yield Explanation
Ans. is 'c' i.e., Hexosaminidase ALipid storage disordersDisorderEnzyme defectGaucher's diseaseb glucosidaseNiemann Pick diseaseSphingomyelinaseFabry's diseasea galactosidaseGM1 gangliosidosisb galactosidaseGM2 gangliosidosisHexosaminidase ASandhoff s diseaseHexosaminidase A and BKrabbe's diseaseGalactosyl ceramidaseMetachromatic leukodystrophyAryl Sulfatase AFarber's diseaseCeramidaseWolman's diseaseAcid lipase

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