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Pediatrics Inborn Errors of Metabolism 3769357b

Only males are affected in:

A
Scheie's syndrome
B
Hunter's syndrome
C
Hurler's syndrome
D
Gaucher's disease
High-Yield Explanation
b. Hunter's syndrome(Ref: Nelson's 20/e p 737-743, Ghai 8/e p 661)As Hunter's disease is a X linked recessive, males are mostly affected by it.

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