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Pediatrics Disorders of Amino acid Metabolism 364e595e

Branched chain keto acids are excreted in urine in:

A
Maple syrup urine disease
B
Hanup disease
C
Albinism
D
Alkaptonuria
High-Yield Explanation
Branched chain keto acids are excreted in urine in: Maple syrup urine disease

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