Pediatrics Inborn Errors of Metabolism 35a48580 Mental retardation is not a feature in this aminoaciduria: A Phenylketonuria B Homocystinuria C Albinism D Maple syrup urine disease High-Yield Explanation c. Albinism(Ref: Nelson's 20/e p 636-642, Ghai 8/e p 653-655)Intellectual disability is common in Phenylketonuria, Homocystinuria and MSUD.