17 yr old pt develops intussusception for which he was operated and the segment showed multiple polyps, the histopathological section is given below. Diagnosis is
High-Yield Explanation
Hamaoma- Tumour like growths composed of mature tissues that are normally present at the site in which they develop.Hamaomatous polyps are juvenile polyps, peutz jeghers, Cronkite Canada syndrome and Cowden syndrome.Patient has peutz Jeghers polyp which is common in adolescent and present with intussusception. Peutz Jeghers syndrome has an autosomal dominant presentation at median age with multiple GI hamaomatous polyps and mucocutaneous pigmentation.Ref: Robbins 8/e p816