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Ophthalmology General 2325247a

Ectopia lentis is seen in all of the following except: March 2007

A
Marfan's syndrome
B
Homocystinuria
C
Weil-Marchesani syndrome
D
Down syndrome
High-Yield Explanation
Ans. D: Down syndrome Ectopia lentis is a displacement or malposition of the eye's crystalline lens from its normal location. More common: Marf an syndrome Homocystinuria Weil-Marchesani syndrome Sulfite oxidase deficiency Hyperlysinemia Less common: Ehlers-Danlos syndrome Crouzon disease Refsum syndrome Sturge-Weber syndrome Pierre Robin syndrome

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