fay Sach's disease is an inborn error of metabolism due to deficiency
High-Yield Explanation
(A) Hexosaminidase-A SPHINGOLIPIDOSESDiseaseEnzyme Deficiency* Tay-sachs diseaseHexosaminidase A* Fabry's diseasea-Galactosidase* Metachromatic leukodystrophyArylsulfatase A* Krabbe's diseaseb-Galactosidase* Gaucher's diseaseb-Glucosidase* Niemann-Pick diseaseSphingomyelinase* Farber's diseaseCeramidase