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Pediatrics Kidney 1f9df3c1

A 9-years-old female child presented with polyuria, polydipsia and metabolic acidosis. On slit lamp examination crystal deposits are seen in cornea. What is the diagnosis?

A
Cystinuria
B
Cystinosis
C
Cystothioninuria
D
Homocysteinuria
High-Yield Explanation
b. Cystinosis(Ref: Nelson 20/e p 2529-2530)Features of renal tubular dysfunction like polyuria, polydipsia and metabolic acidosis, along with presence of crystal deposits in cornea on slit lamp examination of eye suggest a diagnosis of Cystinosis

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