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Biochemistry Phospholipids, Glycolipids and their disorders 1c3d6aad

Metachromatic leukodystrophy is due to deficiency of -

A
Hexosaminidase A
B
Hexosaminidase B
C
Ceramidase
D
Arylsulfatase
High-Yield Explanation
Ans. is 'd' i.e., Arylsulfatase Disease Enzy me deficiencyLipid accumulated Tay-sach diseaseHexosaminidase AGM2 gangliosideSandoff diseaseHexosaminidase BGM2 gangliosideNiemann-Pick diseaseSphingomyelinaseSphingomyelineFarber's diseaseCeramidaseAcyl-sphingosine (ceramide)Fabry's diseasea-galactosidaseGlobotrisylceramideKrabbe's diseaseb-galactosidase (Galactosy lcerami dase)Galactosy lcerami deGaucher's diseaseb-glucosidase (glucocerebrosidase)GlucosylceramideMetachromatic leukodystrophyAry lsulfatase A3-Sulfogalactosylceramide

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