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Biochemistry Phospholipids, Glycolipids and their disorders 1a2079ab

Krabbes disease is due to deficiency of -

A
Sphingomyelinase
B
Beta galactocerebrosidase
C
Hexosaminidase
D
Aryisulfatase
High-Yield Explanation
Ans. is 'b' i.e., Beta gaiactocerebrosidase DiseaseEnzyme deficiencyLipid accumulatedTay-sach diseaseHexosaminidase AGM, gangliosideSandoff diseaseHexosaminidase BGM,gangliosideNiemann-Pick diseaseSphi ngomyel inaseSphingomyelineFarber's diseaseCeram idaseAcyl-sphingosine (ceramide)Fabry's diseasea-galactosidaseGlobotri sy IceramideKrabbe's diseaseb-galactosidase(Galactosylceramidase)GalactosvlceramideGaucher's diseaseb-gl ucosidase (gl ucoccrebrosi dase)Glueosy IceramideMetachromatic leukodystrophyArylsulfatase A3-Suffoga!actosy!ceramide

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