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Pediatrics General 1613cbc7

21-Hydroxylase deficiency - false is ?

A
Most common cause of congenital adrenal hyperlasia
B
Autosomal recessive
C
Femal pseudo hermaphroditism
D
Male pseudo hermephroditism
High-Yield Explanation
Ans. is 'd' i.e., Male pseudo hermephroditism Congenital adrenal hvperplasia (CAH) Group of AR disorder MC adrenal disorder in childhood Most common 21-hydroxylase deficiency =There is elevated level of pregenolone, 17 -OH pergenelone DHEA and decreas level of progesterone, deoxycoisol,and estradiol so 21 hydroxylase deficiency causes female pseudohermaphroditism.

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