Mesencephalo-oculo facial angiomatosis is seen in-

Mesencephalo-oculo facial angiomatosis is seen in Wyburn Mason syndrome. Bonnet-Dechaume-Blanc syndrome, also known asWyburn-Mason syndrome, is a rare congenital disorder characterized by AVM of the brain, retina or facial nevi. It is a pa of spectrum of disease called CAMS(Cerebrofacial aeriovenous metameric syndrome). A & B fundoscopy image showing congestion of vessels at retina consistent with avm. C (T2WI),D(POST CONTRAST T1WI) & E (TOF- MRA) image showing AVM in right basal ganglia in Woburn-mason syndrome.