Male pseudohermaphroditism is seen in –

Male pseudohermaphroditism Genotype is XY External genitalia are female Causes of Male Pseudohermaphroditism A. A defect in testicular differentiation Deletion of the short arm Y chromosome  XY pure gonadal dysgenesis.  Mixed gonadal dysgenesis (MGD). Dysgenetic male pseudohermaphroditism (DMP).   B. A defect in testicular hormone synthesis 1. Leydig cell aplasia 2. Inborn error of testosterone biosynthesis 17-alpha hydroxylase deficiency         17-20 lyase deficiency      17-ketosteroid reductase deficiency. 3 beta-hydroxysteroid dehydrogenase deficiency. 20-22 desmolase deficiency C. A defect in Mullerian inhibiting hormone action D. A defect in androgen action 5-alpha reductase deficiency       Testicular feminization syndrome        Incomplete testicular feminization syndrome Reifenstein syndrome Undetermined etiology True hermaphroditism Both ovarian and testicular tissues are present either in the same (ovotestis) or opposite gonads.